GBE1 Mouse Monoclonal Antibody [Clone ID: OTI4D9]

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SKU
TA500807S
GBE1 mouse monoclonal antibody, clone OTI4D9 (formerly 4D9)
  $200.00
2 Days*
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Specifications
Specifications
Product Data
Clone Name OTI4D9
Application FC, IF, IP, WB
Recommended Dilution WB 1:2000, IF 1:100, FLOW 1:100, IP 2ug/500ul
Reactivity Human, Mouse, Rat
Antibody Host Mouse
Isotype IgG2a
Clonality Monoclonal
Immunogen Full length human recombinant protein of human GBE1 (NP_000149) produced in HEK293T cell.
Buffer PBS (pH 7.3) containing 1% BSA, 50% glycerol and 0.02% sodium azide
Concentration 0.7 mg/ml
Purification Purified from mouse ascites fluids or tissue culture supernatant by affinity chromatography (protein A/G)
Conjugation Unconjugated
Storage Store at -20°C as received.
Stability Stable for 12 months from date of receipt.
Shipping Blue Ice
Predicted Protein Size 80.3 kDa
Gene Name 1,4-alpha-glucan branching enzyme 1
Database Link
Background The protein encoded by this gene is a glycogen branching enzyme that catalyzes the transfer of alpha-1,4-linked glucosyl units from the outer end of a glycogen chain to an alpha-1,6 position on the same or a neighboring glycogen chain. Branching of the chains is essential to increase the solubility of the glycogen molecule and, consequently, in reducing the osmotic pressure within cells. Highest level of this enzyme are found in liver and muscle. Mutations in this gene are associated with glycogen storage disease IV (also known as Andersen's disease). provided by RefSeq
Synonyms APBD; GBE; GSD4
Reference Data
Protein Categories Intracellular Proteins
Protein Families Druggable Genome
Protein Pathways Metabolic pathways, Starch and sucrose metabolism
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Other "OTI4D9" antibodies (4)
SKU Description Size Price
CF500807 Carrier-free (BSA/glycerol-free) GBE1 mouse monoclonal antibody, clone OTI4D9 (formerly 4D9) 100 ug
$620.00
TA500807 GBE1 mouse monoclonal antibody, clone OTI4D9 (formerly 4D9) 100 ul
$447.00
TA500807AM GBE1 mouse monoclonal antibody, clone OTI4D9 (formerly 4D9), Biotinylated 100 ul
$509.00
TA500807BM GBE1 mouse monoclonal antibody, clone OTI4D9 (formerly 4D9), HRP conjugated 100 ul
$509.00

file-alt Citations

Adult Polyglucosan Body Disease: Clinical and histological heterogeneity of a large Italian family
Colombo, Pagliarani, Testolin et al
Neuromuscul. Disord. (2015)
Cited by 17
AI Summary: OriGene’s GBE1 mouse monoclonal antibody (TA500807) was used for Western blot analysis in this study to demonstrate decreased or absent GBE1 protein in muscle tissues of affected patients, supporting the diagnosis of Adult Polyglucosan Body Disease.
Snippet: WB, performed with anti-GBE1 antibody (GBE1 mouse monoclonal antibody TA500807, Origene), showed a decrease of protein on skeletal muscle of patients II-5 /II-6, being protein absent on cardiac muscle of a neonate affected with the congenital variant of glycogenosis ... Cite SaveSaving
WB
Showing 1-1 of 1 papers.
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