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Anti-PEX7 Antibody EPR7714(2)(B)
Also for PEX7 (NM_000288)
|A synthetic peptide corresponding to residues in human PEX7 was used as an immunogen.|
|Mouse, Rat, Human
||Lot dependent; please refer to CoA along with shipment
||WB: 1:1000 - 1:10000
|Preservative: 0.01% Sodium azide|
Constituents: 50% Glycerol, 0.05% BSA
|Tissue culture supernatant
|Is unsuitable for Flow Cyt,ICC/IF,IHC-P or IP.
|Homo sapiens peroxisomal biogenesis factor 7 (PEX7)|
|PBD9B; PTS2R; RCDP1; RD|
|PEX7 is the cytosolic receptor for the set of peroxisomal matrix enzymes targeted to the organelle by the peroxisome targeting signal 2 (PTS2). Defects in PEX7 cause peroxisome biogenesis disorders (PBDs), which are characterized by multiple defects in peroxisome function. There are at least 14 complementation groups for PBDs, with more than one phenotype being observed in cases falling into particular complementation groups. Although the clinical features of PBD patients vary, cells from all PBD patients exhibit a defect in the import of one or more classes of peroxisomal matrix proteins into the organelle. Defects in PEX7 have been associated with PBD complementation group 11 (PBD-CG11) disorders, rhizomelic chondrodysplasia punctata type 1 (RCDP1), and Refsum disease (RD) (1).|
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Western blot - Anti-PEX7 antibody; All lanes : Anti-PEX7 antibody [EPR7714(2)(B)] at 1/1000 dilution.Lane 1 : Fetal muscle lysate.Lane 2 : MCF7 lysate.Lysates/proteins at 10 ug per lane.Secondary.HRP labelled goat anti-rabbit at 1/2000 dilution.Predicted band size : 36 kDa.Observed band size : 36 kDa.