Ornithine Carbamoyltransferase (OTC) (NM_000531) Human Untagged Clone
CAT#: SC119821
OTC (untagged)-Human ornithine carbamoyltransferase (OTC), nuclear gene encoding mitochondrial protein
"NM_000531" in other vectors (6)
Product Images
Specifications
Product Data | |
Type | Human Untagged Clone |
Tag | Tag Free |
Symbol | Ornithine Carbamoyltransferase |
Synonyms | OCTD; OTCD |
Vector | pCMV6-XL4 |
E. coli Selection | Ampicillin (100 ug/mL) |
Mammalian Cell Selection | None |
Sequence Data |
>OriGene ORF within SC119821 sequence for NM_000531 edited (data generated by NextGen Sequencing)
ATGCTGTTTAATCTGAGGATCCTGTTAAACAATGCAGCTTTTAGAAATGGTCACAACTTC ATGGTTCGAAATTTTCGGTGTGGACAACCACTACAAAATAAAGTGCAGCTGAAGGGCCGT GACCTTCTCACTCTAAAAAACTTTACCGGAGAAGAAATTAAATATATGCTATGGCTATCA GCAGATCTGAAATTTAGGATAAAACAGAAAGGAGAGTATTTGCCTTTATTGCAAGGGAAG TCCTTAGGCATGATTTTTGAGAAAAGAAGTACTCGAACAAGATTGTCTACAGAAACAGGC TTTGCACTTCTGGGAGGACATCCTTGTTTTCTTACCACACAAGATATTCATTTGGGTGTG AATGAAAGTCTCACGGACACGGCCCGTGTATTGTCTAGCATGGCAGATGCAGTATTGGCT CGAGTGTATAAACAATCAGATTTGGACACCCTGGCTAAAGAAGCATCCATCCCAATTATC AATGGGCTGTCAGATTTGTACCATCCTATCCAGATCCTGGCTGATTACCTCACGCTCCAG GAACACTATAGCTCTCTGAAAGGTCTTACCCTCAGCTGGATCGGGGATGGGAACAATATC CTGCACTCCATCATGATGAGCGCAGCGAAATTCGGAATGCACCTTCAGGCAGCTACTCCA AAGGGTTATGAGCCGGATGCTAGTGTAACCAAGTTGGCAGAGCAGTATGCCAAAGAGAAT GGTACCAAGCTGTTGCTGACAAATGATCCATTGGAAGCAGCGCATGGAGGCAATGTATTA ATTACAGACACTTGGATAAGCATGGGACAAGAAGAGGAGAAGAAAAAGCGGCTCCAGGCT TTCCAAGGTTACCAGGTTACAATGAAGACTGCTAAAGTTGCTGCCTCTGACTGGACATTT TTACACTGCTTGCCCAGAAAGCCAGAAGAAGTGGATGATGAAGTCTTTTATTCTCCTCGA TCACTAGTGTTCCCAGAGGCAGAAAACAGAAAGTGGACAATCATGGCTGTCATGGTGTCC CTGCTGACAGATTACTCACCTCAGCTCCAGAAGCCTAAATTTTGA Clone variation with respect to NM_000531.5 >OriGene 5' read for NM_000531 unedited
NAAGTTCACATTTGTATACGACTCACTATAGGCGGCCGCGAATTCGCACGAGGGGACTTT GATAAGGAAGCTGAAGGGTGATATTACCTTTGCTCCCTCACTGCAACTGAACACATTTCT TAGTTTTTAGGTGGCCCCCGCTGGCTAACTTGCTGTGGAGTTTTCAAGGGCATAGAATCG TCCTTTACACAATTAAAAGAAGATGCTGTTTAATCTGAGGATCCTGTTAAACAATGCAGC TTTTAGAAATGGTCACAACTTCATGGTTCGAAATTTTCGGTGTGGACAACCACTACAAAA TAAAGTGCAGCTGAAGGGCCGTGACCTTCTCACTCTAAAAAACTTTACCGGAGAAGAAAT TAAATATATGCTATGGCTATCAGCAGATCTGAAATTTAGGATAAAACAGAAAGGAGAGTA TTTGCCTTTATTGCAAGGGAAGTCCTTAGGCATGATTTTTGAGAAAAGAAGTACTCGAAC AAGATTGTCTACAGAAACAGGCTTTGCACTTCTGGGAGGACATCCTTGTTTTCTTACCAC ACAAGATATTCATTTGGGTGTGAATGAAAGTCTCACGGACACGGCCCGTGTATTGTCTAG CATGGCAGATGCAGTATTGGCTCGAGTGTATAAACAATCAGATTTGGACACCCTGGCTAA AGAAGCATCCATCCCAATTATCAATGGGCTGTCAGATTTGTACCATCCTATCCAGATCCT GGCTGATTACCTCACGCTCCAGGAACACTATAGCTCTCTGAAAGGTCTTACCCTCAGCTG GATCGGGGATGGGAACAATATCCTGCACTCCATCATGATGAGCGCAGCGAAATTTCGAAT GCACCTTNCAGCAGCTACTCCAAAGGGTTATGAGCCGATGCTAGTGTAACCAAGTTGGGC AGGCAGTATGCCAAAGAGAATGC >OriGene 3' read for NM_000531 unedited
NTTACTCTGNNACCGCGGCCGCATNCTANGATCGAGTTTTTTTTTTTTTTTTTTTTTAGG TGACAGGATTTATTATGTACACCAAAGATGCAAGCGTCATTTCTAGAATTTTCGTTAAAC TTCGGAGTTGTAATAGCTATATAGGAAAAGGGGTAAGAAGAAAGAGGAGATGAAAACAGC TTTGCAAAAGTTAAGGGTGAATTTTCCTCCCCTATTTTCTTTTTTCCTGACAATATAAAT AATGTCTGATTAAGATGAAAAGTTAAGAAAGCAAATACATTCCTACAGAATTGGGCTGAG AATGAGGTTAAATTGTATGTACACAATAAAGAAAGCTATAGAGCTTTTTGAGGAAAAAAT GACTATATTTTGGCAAGAAAATTATTACAAGTTCTTTCCAAGTGAGGGAAGAAGACTATA CCATCCATTTAGTTCAAAGAATAACCAGGAATGAGATGGGAGCTCGTTACTATGGCAGAC CATTTGGCAAGTGGAAGAACACTTCTTTCTATGTAGGCAATTTGAGGGTGAGCCTTCCAC AATCCATATGACACCTTGTTCTACTCTCTGCTGAAAGATATTCCACTAAACTCCACTCTC TTTCTAAGTGCTTCCAATAAATTACTATGGACACAAAAGTCACCTTTGACATTTACTGGA AAATTTGATGTTTTTTTCTGTAACATTATGAGCCTCTTTCCCCCACAAAAAATGTTTTAT TGCACCTTCATTGCAAATCTAATTTGTAATTCATCCCTTGCTTACTCATTTAAGTCAGAG CTGTGTGCTGAAGAATATCAGTCAACCAGCCTGGAAACATTNTTCTAATAGTAAATGTAG AATGGTAAGGAAATACATTATTNTGTCTTCTGTAAATGTATAATTTTTAAAAAACTTCAC TATGTTATTTACATTNNTACTANNAATCAATATTCATATATTCACATACAATG |
Restriction Sites | NotI-NotI |
ACCN | NM_000531 |
Insert Size | 2800 bp |
OTI Disclaimer | Our molecular clone sequence data has been matched to the reference identifier above as a point of reference. Note that the complete sequence of our molecular clones may differ from the sequence published for this corresponding reference, e.g., by representing an alternative RNA splicing form or single nucleotide polymorphism (SNP). |
Product Components | The ORF clone is ion-exchange column purified and shipped in a 2D barcoded Matrix tube containing 10ug of transfection-ready, dried plasmid DNA (reconstitute with 100 ul of water). |
Reconstitution | 1. Centrifuge at 5,000xg for 5min. 2. Carefully open the tube and add 100ul of sterile water to dissolve the DNA. 3. Close the tube and incubate for 10 minutes at room temperature. 4. Briefly vortex the tube and then do a quick spin (less than 5000xg) to concentrate the liquid at the bottom. 5. Store the suspended plasmid at -20°C. The DNA is stable for at least one year from date of shipping when stored at -20°C. |
Reference Data | |
RefSeq | NM_000531.3, NP_000522.3 |
RefSeq Size | 1927 bp |
RefSeq ORF | 1065 bp |
Locus ID | 5009 |
UniProt ID | P00480 |
Cytogenetics | Xp11.4 |
Domains | OTCace, OTCace_N |
Protein Families | Druggable Genome |
Protein Pathways | Arginine and proline metabolism, Metabolic pathways |
Gene Summary | This nuclear gene encodes a mitochondrial matrix enzyme. Missense, nonsense, and frameshift mutations in this enzyme lead to ornithine transcarbamylase deficiency, which causes hyperammonemia. Since the gene for this enzyme maps close to that for Duchenne muscular dystrophy, it may play a role in that disease also. [provided by RefSeq, Jul 2008] |
Documents
Product Manuals |
FAQs |
SDS |
Resources
Other Versions
SKU | Description | Size | Price |
---|---|---|---|
RC214662 | OTC (Myc-DDK-tagged)-Human ornithine carbamoyltransferase (OTC), nuclear gene encoding mitochondrial protein |
USD 457.00 |
|
RC214662L1 | Lenti ORF clone of Human ornithine carbamoyltransferase (OTC), nuclear gene encoding mitochondrial protein, Myc-DDK-tagged |
USD 757.00 |
|
RC214662L2 | Lenti ORF clone of Human ornithine carbamoyltransferase (OTC), nuclear gene encoding mitochondrial protein, mGFP tagged |
USD 757.00 |
|
RC214662L3 | Lenti ORF clone of Human ornithine carbamoyltransferase (OTC), nuclear gene encoding mitochondrial protein, Myc-DDK-tagged |
USD 757.00 |
|
RC214662L4 | Lenti ORF clone of Human ornithine carbamoyltransferase (OTC), nuclear gene encoding mitochondrial protein, mGFP tagged |
USD 757.00 |
|
RG214662 | OTC (tGFP-tagged) - Human ornithine carbamoyltransferase (OTC), nuclear gene encoding mitochondrial protein |
USD 657.00 |
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